Bird Flu (Avian Influenza) Pandemic, the Cytokine Storm: What Drugs Work and Don't Work

What is a Cytokine Storm?viruses containing a combination of genes from a
human influenza virus and an avian influenza virus. The
A cytokine storm, also called "systemic inflammatoryorigin of the 1918-19 pandemic virus is not clear, but if
response syndrome" (SIRS) is the systemicits origin was in China as suspected, it could have
expression of a healthy and vigorous immune systemsimilarly been caused by a genetic recombination of
resulting in the release of more than 150human and avian influenza viruses. This can more
inflammatory mediators (cytokines, oxygen freeeasily occur if humans are in close proximity to both
radicals, and coagulation factors). Bothlive birds and pigs, as can occur in public markets in
pro-inflammatory cytokines (such as Tumor NecrosisAsia. Osterholm reports the last influenza pandemic
Factor-alpha, InterLeukin-1, and InterLeukin-6) and(1968) occurred 37 years ago, emerging in China. At
anti-inflammatory cytokines (such as interleukin 10,that time China's human population was 790 million, its
and interleukin 1 receptor antagonist) are elevated inpig population was 5.2 million, and its poultry
the serum, and the fierce and often lethal interplaypopulation was 12.3 million. Today, these populations
of these cytokines is referred to as a "Cytokinenumber 1.3 billion, 508 million, and 13 billion,
Storm". The primary contributors to the cytokinerespectively. The human and animal populations of
storm are TNF-a (Tumor Necrosis Factor-alpha) andother Asian countries have similarly increased
IL-6 (Interleukin-6). The cytokine storm is anexponentially, which has increased the chances for
inappropriate (greatly exaggerated) immune responseclose contact between birds, pigs and humans in
that is caused by rapidly proliferating and highlythese countries, creating optimal conditions for the
activated T-cells or natural killer (NK) cells. These cellsemergence of new viruses, such as the H5N1
are themselves activated by infected macrophages.subtype. On August 12, 2004, the Vietnamese
The cytokine storm must be treated and suppressedMinistry of Health reported three confirmed human
or lethality can result.deaths to the World Health Organization (WHO) from
Acute respiratory viral infection results in a cytokineconfirmed avian influenza H5 infection. If the virus is
storm effecting the lungs, and subsequent damageconfirmed to belong to the same H5N1 strain that
to alveoli and lung tissue results in the lethality seen incaused 22 cases (15 deaths) in Vietnam and 12 cases
more severe flu viral infections, especially those(8 deaths) in Thailand in 2005, and human-to-human
fatalities among young healthy adults.contact versus human to bird or human-to-swine
In the absence of prompt medical intervention tocontact is suspected, this may indicate that H5N1 has
stop the "cytokine storm", the lung will sufferadapted to the point that it is transmissible and has
permanent damage. Many of these patients willthe potential to cause the next pandemic. In May
develop acute respiratory distress syndrome (ARDS),2006, it was reported that a family of 7 died of the
i.e. will present with pulmonary edema that is notbird flu after having no detectible contact with an
caused by volume overload, or a depressed leftinfected bird. If this is the case, the virus may have
ventricular function. Deaths will usually result fromundergone a final mutation giving it the potential to
multisystem organ failure, and not from lung failure.cause a pandemic. What Are the Symptoms of the
Sepsis, Viral Infections, and Cytokine StormBird Flu: Initial Presentaion of Influenza A (H5N1) Avian
Sepsis is a severe systemic inflammatory responseInfluenza:
and is one example of a pathologic condition- Pulmonary: Radiographically confirmed pneumonia,
associated with "cytokine storm". Sepsis is an oftenacute respiratory distress syndrome (ARDS), or
lethal hemodynamic collapse which is usually the resultother severe respiratory illness for which an alternate
of a super infection by gram-negative bacterialdiagnosis cannot be established
endotoxins. Sepsis is also classified as septic shock- One or more of the following: cough and/or sore
syndrome (SSS).throat and/or shortness of breath, AND a history of
Cytokine storm can also result from viral infectionscontact with poultry (e.g., visited a poultry farm, a
such as influenza, and an exaggerated systemichousehold raising poultry, or a bird market) or contact
immune response to that particular viral infectionwith a known or suspected human case of influenza
(designated a type A, subtype "H1N1" virus) mayA (H5N1) in an H5N1-affected country within 10 days
have been the cause of high lethality seen in theof symptom onset.
influenza pandemic of 1918 to 1919. The great- Dyspnea
influenza pandemic was the most destructive- Fever (temperature of >38°C or
pandemic in recorded world history, and killed more>100.4°F)
people (estimated between 20 to 50 million) than allSymptoms Of The Cytokine Storm:
casualties resulting from the first World War.The end stage, or final result, of cytokine storm
Although the Spanish Flu pandemic affected an(SIRS) or sepsis is multiple organ dysfunction
enormous percentage of the world wide populationsyndrome (MODS). The end-stage symptoms of the
(up to 20% of the world population according tobird flu, or other infection precipitating the cytokine
some sources), and killed between 20 and 50 millionstorm may include:
persons, no more than 5% of the people who- hypotension
contracted the Spanish Flu died (Brown et. al- tachycardia
reported the highest death rate in India at 50 deaths- dyspnea
per 1000 persons contracting the disease, or a five- fever (temperature of >38°C or
percent fatality rate). After 218 human cases of>100.4°F)
avian influenza (bird flu) have been confirmed- Ischemia, or insufficient tissue perfusion (especially
world-wide (as of May, 2006), the lethality rateinvolving the major organs)
stands at 57%. Should this strain develop into a- uncontrollable hemorrhage
pandemic, and should it keep its current mortality- and multisystem organ failure (caused primarily by
rate, it has the potential to be 10 times more lethalhypoxia, tissue acidosis, and severe metabolism
than the 1918 pandemic.dysregulation
Is the World Health Organization AdequatelyOxygen free radicals, histamine, complement factor
Defending against a Potential Pandemic of AvianC5a, Beta-endorphin, thromboxane B2, and platelet
Influenzaactivating factor are implicated in SSS. The major
Avian Influenza (also called the "Bird flu") currently ispro-inflammatory cytokines which are implicated in
10 times more lethal than the strain of Spanish FluSSS are TNF-alpha, IL1, IL6 and IL8. Serum TNF alpha
that caused the great influenza pandemic of 1918 andconcentrations in excess of 1 ng/mL are frequently
killed up to 50 million people world-wide, and it couldpredictive of a lethal outcome, however serum
become the most lethal flu pandemic of all history ifconcentrations of other inflammatory cytokines
the virus mutates allowing it to be more easilyinvolved in the pathophysiology of Septic shock are
passed from person to person. Bird Flu patients dieusually not reliable predictors of the severity of the
from acute respiratory distress syndrome (ARDS)shock state or clinical outcome. These cytokines are
caused by the "cytokine storm", and NOT directlyreleased by macrophages following activation by
from the virus. Neuraminidase inhibitors (i.e. Tamiflu,bacterial endotoxins.
Relenza) are not proven effective for bird fluPreventing and/or treating the cytokine storm
patients, although they have been recommended byassociated with influenza with antiviral medications,
the World Health Organization for this use, areprescription medications and vaccines that are
currently used to treat almost all bird flu patients, andapproved (or may soon be approved) by the U.S.
are being stockpiled by governments world-wideFood and Drug Administration (FDA):
(including the United States) to treat a potential- Acambis Biotechnology Vaccine: Acambis announced
pandemic should the avian influenza virus undergo aon August 4, 2005 that it has entered into
final mutation which would allow it to be more easilycollaboration with a Belgian research centre to
passed from person to person. A treatment todevelop a single-dose flu vaccine that could offer
prevent or reduce the autoimmune reaction (cytokinepermanent protection against all strains of both
storm) associated with the bird flu is commerciallyinfluenza A and influenza B, potentially offering
available by prescription, but is not currently beingprotection against future influenza pandemics.
recommended by the World Health Organization to- ACE inhibitors and Angiotensin II Receptor Blockers
treat these patients.(ARBs) make sense in the treatment of, and have
Influenza A, The most lethal influenza and theproven to be beneficial in treating the cytokine storm
precursor of all Pandemic Viruses(the major cause of lethality in Bird Flu) of SARS. See
Influenza viruses responsible for causing pandemicsalso: PUBMED, The cytokine storm and the
are influenza type A viruses which emerge as a resultrenin-angiotensin-aldosterone system.
of a process called "antigenic shift". Antigenic shift- Amantadine (Brand name Symmetrel: Treatment of
causes an abrupt or sudden, major change in certaininfluenza type A-2, but not type B). This drug cannot
proteins on the surface of the influenza A virustreat the cytokine storm associated with avian
(specifically the hemagglutinin or "HA" protein and theinfluenza, and has not been tested in patients with
neuraminidase or the "NA" protein).Certain antigenicthe bird flu.
shifts may allow the virus to become more easily- Aventis Vaccine: Preliminary research suggests the
transmissible, more "contagious". Once this type ofinfluenza A vaccine developed by Sanofi-Aventis is
shift occurs, wide-spread infection usually followseffective against H5N1 avian flu virus. The NIH (US
quickly. Antigenic shift is most dangerous when itNational Institutes of Health) reported on August 5,
occurs in a virus that has demonstrated high lethality,2005 (New York Times) that preliminary tests have
such as the H5N1 bird flu.confirmed that an experimental vaccine in
History has recorded 10 pandemics of influenza A indevelopment by Sanofi-Aventis Pharmaceutical
the past 300 years. The sudden appearance of newCompany appears to be effective in preventing
influenza A virus subtypes during the 20th centuryinfection with the bird flu (avian influenza virus).
has caused three pandemics, all of which spreadResearchers believe that the avian influenza virus, an
world-wide within 1 year of first being detected.influenza type-A, subtype H5N1, could trigger the
Influenza Pandemics of the 20th Centurynext worldwide flu pandemic.
- 1918-19, "Spanish flu," [Type A, subtype (H1N1)],- Oseltamivir (Brand name Tamiflu: a neuraminidase
caused the highest number of known influenzainhibitor for treatment or prevention of both influenza
deaths: more than one-half million people died withintype A and B, indicated for use within 2 days of
the United States (nearly half of the deaths weresymptoms). This drug cannot treat the cytokine
young healthy adults aged 20-40), and between 50storm associated with avian influenza, and has not
and 100 million people may have died worldwide. Mostbeen tested in patients with the bird flu. Most of the
deaths occurred within the first few days afteravian flu victims in SE Asia and Turkey received
infection, some deaths within hours of symptomTamiflu, and still suffered mortality rates exceeding
onset, and other deaths occurred later as a result of50%. Tamiflu has been declared "ineffective" against
complications. Influenza A (H1N1) viruses still circulatethe bird flu by a physician who has personally used
today after having been reintroduced in the 1970s.the drug to treat 41 bird flu patients (19% of all
Although called the "Spanish Flu" because the firstreported cases to date).
widely reported deaths were in Spain, it probably- Prednisone and corticosteroids: Treatment of active
originated in China.disease may involve the use of corticosteroids.
- 1957-58, "Asian flu," [Type A, subtype (H2N2)],- Rimantadine (Brand name Flumadine: Treatment of
caused about 70,000 deaths in the United States.influenza type A, but not B). This drug cannot treat
The "asian flu" was initially identified in China in latethe cytokine storm associated with avian influenza,
February 1957. Three months later, it spread to theand has not been tested in patients with the bird flu.
United States with early reports of infection as early- Zanamivir (Brand name Relenza: a neuraminidase
as June 1957.inhibitor for treatment of both influenza type A and
- 1968-69, " Hong Kong flu," [Type A subtypetype B, indicated for use within 2 days of
(H3N2)], was responsible for about 34,000 deaths insymptoms). This drug cannot treat the cytokine
the United States. The "Hong Kong flu" virus wasstorm associated with avian influenza, and has not
first detected in Hong Kong in early 1968 and spreadbeen tested in patients with the bird flu. Most of the
to the United States within a few months. Influenzaavian flu victims in SE Asia and Turkey received
A (H3N2) viruses still circulate today. Both theTamiflu (a drug similar to Relenza), and still suffered
1957-58 and 1968-69 pandemics were caused bymortality rates exceeding 50%.